Relatives of patients with the possibly hereditary forms of renal tubular acidosis should be tested.

The prognosis is good for someone who has renal tubular acidosis and they are receiving the right treatments. They will need high doses of bicarbonate and correction of the acidosis and potassium levels are required.

Proximal renal tubular acidosis (type 2) is caused by hereditary diseases, such as Fanconi's syndrome, fructose intolerance, and Lowe's syndrome.

Type 4 renal tubular acidosis is not hereditary, but is associated with diabetes mellitus, sickle cell anemia, an autoimmune disease, or an obstructed urinary tract.

Type I Renal Tubular Acidosis