Sucrose intolerance: Information from Answers.com


Sucrose intolerance
Classification and external resources
Sucrose
ICD-10	E 74.3
ICD-9	271.3
OMIM	222900
DiseasesDB	29844

Sucrose intolerance, also called Congenital Sucrase-Isomaltase Deficiency (CSID)^[1] or Sucrase-isomaltase deficiency,^[2] is the condition in which sucrase, an enzyme needed for proper metabolization of sucrose, is not produced in the small intestine.

It is more common among the Inupiat.^[3]

1 Presentation
2 References
3 See also
4 External links

Presentation

The result of consuming sucrose is excess gas production and often diarrhea and malabsorption.

References

^ Sander P, Alfalah M, Keiser M, et al. (January 2006). "Novel mutations in the human sucrase-isomaltase gene (SI) that cause congenital carbohydrate malabsorption". Hum. Mutat. 27 (1): 119. doi:10.1002/humu.9392. PMID 16329100.
^ Baudon JJ, Veinberg F, Thioulouse E, Morgant G, Aymard P, Charritat JL (April 1996). "Sucrase-isomaltase deficiency: changing pattern over two decades". J. Pediatr. Gastroenterol. Nutr. 22 (3): 284–8. PMID 8708882. http://meta.wkhealth.com/pt/pt-core/template-journal/lwwgateway/media/landingpage.htm?issn=0277-2116&volume=22&issue=3&spage=284.
^ Meier RJ, Draper H, Milan F (January 1991). "Pedigree analysis of sucrose intolerance among Native Alaskans". Arctic Med Res 50 (1): 8–12. PMID 2021397.

External links

Digestive system · Digestive disease · Gastroenterology (primarily K20-K93, 530-579)

Upper GI tract

Intestinal/
enteropathy

Small intestine/ (duodenum/jejunum/ileum)	Enteritis (Duodenitis, Jejunitis, Ileitis) — Peptic (duodenal) ulcer (Curling's ulcer) — Malabsorption: Coeliac · Tropical sprue · Blind loop syndrome · Whipple's · Short bowel syndrome · Steatorrhea · Milroy disease

Large intestine (appendix/colon)	Appendicitis · Colitis (Pseudomembranous, Ulcerative, Ischemic, Microscopic, Collagenous, Lymphocytic) · Functional colonic disease (IBS, Intestinal pseudoobstruction/Ogilvie syndrome) — Megacolon/Toxic megacolon · Diverticulitis/Diverticulosis

Large and/or small	Enterocolitis (Necrotizing) · IBD (Crohn's disease) — vascular: Abdominal angina · Mesenteric ischemia · Angiodysplasia — Bowel obstruction: Ileus · Intussusception · Volvulus · Fecal impaction — Constipation · Diarrhea (Infectious)

Rectum	Proctitis (Radiation proctitis) · Proctalgia fugax · Rectal prolapse

Anus	Anal fissure/Anal fistula · Anal abscess · Anal dysplasia · Pruritus ani

Accessory

Liver	Hepatitis (Viral hepatitis, Autoimmune hepatitis, Alcoholic hepatitis) · Cirrhosis (PBC) · Fatty liver (NASH) · vascular (Hepatic veno-occlusive disease, Portal hypertension, Nutmeg liver) · Alcoholic liver disease · Liver failure (Hepatic encephalopathy, Acute liver failure) · Liver abscess (Pyogenic, Amoebic) · Hepatorenal syndrome · Peliosis hepatis

Gallbladder	Cholecystitis · Gallstones/Cholecystolithiasis · Cholesterolosis · Rokitansky-Aschoff sinuses · Postcholecystectomy syndrome

Bile duct/ other biliary tree	Cholangitis (PSC, Secondary sclerosing cholangitis, Ascending) · Cholestasis/Mirizzi's syndrome · Biliary fistula · Haemobilia · Gallstones/Cholelithiasis common bile duct (Choledocholithiasis, Biliary dyskinesia)

Pancreatic	Pancreatitis (Acute, Chronic, Hereditary) · Pancreatic pseudocyst · Exocrine pancreatic insufficiency · Pancreatic fistula

Hernia

Diaphragmatic: Congenital diaphragmatic · Hiatus — Abdominal hernia: Inguinal (Indirect, Direct) · Umbilical · Incisional · Femoral — Obturator hernia · Spigelian hernia · Internal hernia

Peritoneal

Peritonitis (Spontaneous bacterial peritonitis) · Hemoperitoneum · Pneumoperitoneum

GI bleeding/BIS

Upper (Hematemesis, Melena) · Lower (Hematochezia)

See also: congenital and neoplasia

Inborn error of carbohydrate metabolism: monosaccharide metabolism disorders (including glycogen storage diseases) (E73-74, 271)

Sucrose, transport
(extracellular)

Disaccharide catabolism	Lactose intolerance · Sucrose intolerance

Monosaccharide transport	Glucose-galactose malabsorption · Inborn errors of renal tubular transport (Renal glycosuria)

Hexose → glucose

Monosaccharide catabolism

fructose: Essential fructosuria · Fructose intolerance
galactose/galactosemia : GALK deficiency · GALT deficiency/GALE deficiency

Glucose ⇄ glycogen

Glycogenesis	GSD type 0, glycogen synthase · GSD type IV, Andersen's, branching

Glycogenolysis	extralysosomal: GSD type V, McArdle, muscle glycogen phosphorylase/GSD type VI, Hers', liver glycogen phosphorylase · GSD type III, Cori's, debranching lysosomal/LSD: GSD type II, Pompe's, glucosidase

Glucose ⇄ CAC

Glycolysis	MODY 2 · GSD type VII, Tarui's, phosphofructokinase · Triosephosphate isomerase deficiency · Pyruvate kinase deficiency

Pyruvate catabolism	PDHA · Fumarase deficiency

Gluconeogenesis	PCD · Fructose bisphosphatase deficiency · GSD type I, von Gierke, glucose 6-phosphatase

Pentose phosphate pathway

Glucose-6-phosphate dehydrogenase deficiency · Pentosuria

Other

Hyperoxaluria (Primary hyperoxaluria)

see also fructose and galactose metabolism enzymes, intermediates; see also glycolysis enzymes, intermediates
see also glycogenesis and glycogenolysis enzymes, intermediates; see also pentose phosphate pathway enzymes, intermediates

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Sucrose intolerance

Contents

Presentation

References

See also

External links