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What is Huntington Chorea disease?

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2008-06-18 09:11:47
2008-06-18 09:11:47

Dr. George Huntington of Long Island, New York first described this disease in 1872. Huntington's Chorea is inherited, degenerative disorder of the Central Nervous System caused by a dominant gene. If one person's parents has developed this disease there is a 50% chance their children will inherit it. The symptoms generally start around 35 years of age, but can onset later. This disease causes dysfunctional movements (often referred too as 'clumsiness' in it's earlier stages), but as the disease progresses the movements of the person become uncontrollable. The movements and body postures appear bizarre. Other symptoms include: Forgetfulness; irritability and as the disease progresses dementia, memory loss and severe anger outbursts as well as lack of reasoning. Patients suffering from Huntington's Chorea show degenerative changes in the basal ganglia structures, which ultimately result in a severely shrunken brain and enlarged ventricles. The symptoms are caused by a significant reduction in volume and activity of two principle neurotransmitters (naturally occurring chemicals in the brain) called Acetylcholine and GABA and, in turn affecting the activity of the neurotransmitter Dopamine which becomes hyperactive. Medications can ease the symptoms (including the use of dopamine antagonists or neuroleptics) but, there may be severe side effect. There is no cure for Huntington's Chorea. However, new techniques involving neural grafting (implanting healthy fetal brain cells into the damaged area) may offer hope for the sufferer in the near future. This disease may continue relentlessly for 10 to 20 years and cause of death is commonly Heart disease after a severe illness or due to falls or choking. There is hope! Scientists are getting closer to a cure for this disease and in the near future they will be advanced treatments and medications.

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This is because about 90% of people with HD have chorea. These movements may be mild at first, but can worsen and become more involuntary with time.


Huntington disease is also called Huntington chorea, from the Greek word for "dance," referring to the involuntary movements that develop as the disease progresses. It is occasionally referred to as "Woody Guthrie disease" for the American folk singer who died from it. Huntington disease (HD) causes progressive loss of cells in areas of the brain responsible for some aspects of movement control and mental abilities. A person with HD gradually develops abnormal movements and changes in cognition (thinking), behavior and personality.


The areas of the body most commonly affected by chorea are the face, limbs, and trunk. As the chorea progresses, breathing, swallowing, and the mouth and nasal muscles may become involved.


huntington's Disease was first recognised as an inherited disorder in 1872 when a 22-year-old American doctor, George Huntington, wrote a paper called On Chorea. His paper was later published in the Medical and Surgical Reporter of Philadelphia and the disorder he described became known as Huntington's Chorea.


to benefit some patients with HD by controlling the involuntary movements of chorea. It works by lowering the levels of dopamine and other neurotransmitters in the brain.


AnswerHuntington's Disease and Huntington's Chorea are essentially one and the same. Chorea is a greek term used to define the uncontrollable movements a person might have with any number of neurological diseases. Huntington's Disease is what took his life.


Sydenham's chorea is a disorder that occurs in children and is associated with rheumatic fever.


Chorea Huntington, phenylketonuria, sickle cell anemia, down syndrome, ...


dystonia, or sustained abnormal postures, including facial grimaces, a twisted neck, or an arched back; chorea, in which involuntary jerking, twisting or writhing motions become pronounced


He is the first person that described the Huntington disease.


Yes. The involuntary movements of Huntington's were thought to resemble a kind of dance (chorea - like choreograph).


A common name for chorea. As to the cause of chorea nothing definite is known. There are certain reasons for believing that in many cases it is a disease of the brain.


Huntingdons chorea is caused by a dominant allele.


There IS no microbe. HD is a genetically transmitted disease- you can't catch it.





Huntington's is a neurological disease that affects the brain.


Chorea is an old name for Huntington's Disease. It is genetically transmitted from parent to child. The only way to get HD is to inherit the gene that causes it from one of your parents that also had HD.


He discovered genes causing cystic fibrosis, neurofibromatosis, and Huntington Chorea. (i would spell check this answer) please look to further references.


huntington's chorea:it's an autosomal dominant inherited diseaseit causes the degeneration of neurons mainly in caudate nucleus, which then will cause the widening of anterior horns of your lateral ventriclessyndenham's chorea:it might affect children suffering from rheumatic feverinvoluntary movements are transient and followed by full recovery


No but it is a very slow and unpainful processno sadly huntingtons disease(also known as huntingtons chorea) has no known cure.


Its Passed On From Your Parents Its Inherited


Huntington's is a genetically transmitted disease- you get it by inheriting the gene for it.


chorea, it attacks the nervous system and causes someone to shake uncontrollably



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