a congenital brain malformation involving the cerebellum and the
fluid filled spaces around it. A key feature of this syndrome is
the partial or even complete absence of the part of the brain
located between the two cerebellar hemispheres (cerebellar vermis).
The Dandy-Walker complex is a genetically sporadic disorder that
occurs one in every 25,000 live births, mostly in females.
http://en.wikipedia.org/wiki/Dandy-Walker_syndrome