An extremely rare disease (28 families worldwide), transmitted by a dominant inherited gene based on the mutation of a prion that forms plaques similar to BSE (Bovine Spongiform Encephalopathy) and CJD (Cruetzfeldt-Jakob Disease). The patient experiences panic attacks, phobias, and hallucinations, loses weight, and then dies. It is considered a Transmittable Spingiform Encephalopathy (TSE).
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