It is an organic acid produced from carbohydrate.

Alpha-imino-glutaric acid. The imino stands for a C=N double bond.

GAT1 is a congenital defect that manifests by the patient not being able to break down certain amino acids.

There are hundreds of them. Amino acidopathies and organic acidemias, resulting from disorders in amino or fatty acid catabolism, Dysfunction of the enzyme glutaryl CoA dehydrogenase prevents the metabolism of tryptophan, hydroxylysine, and lysine, resulting in increased urine glutaric acid metabolites, and cerebral organic acidopathies resulting from defects in the leucine catabolic pathway among many more.