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Mannosidosis is an inherited metabolic disorder caused by deficiency of the enzyme mannosidase in your body.

There are two types:

  • Alpha-mannosidosis
  • Beta-mannosidosis

More detailed information can be found on Wikipedia.

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Related answers

Mannosidosis is an inherited metabolic disorder caused by deficiency of the enzyme mannosidase in your body.

There are two types:

  • Alpha-mannosidosis
  • Beta-mannosidosis

More detailed information can be found on Wikipedia.

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Defective Enzyme Disorder: includes the following:

α-Mannosidosis α-Mannosidase β-Mannosidosis β-Mannosidase

α-Fucosidosis α-Fucosidase

Sialidosis α-Neuraminidase

Galactosialidosis Protective protein

Aspartylglucosaminuria Aspartylglycosaminidase

Schindler disease α-N-Ac-galactosaminidase

Mucolipidosis II (I-cell disease) N-acetylglycosmaine-1 phosphotransferase

Mucolipidosis III N-acetylglycosmaine-1- phosphotransferase.

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