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What else can I help you with?
How is Wilson disease treated?
Wilson disease is typically treated with medications that help remove excess copper from the body, such as chelating agents like D-penicillamine and trientine. A low-copper diet is also recommended, limiting foods high in copper like liver and shellfish. In severe cases, liver transplant may be necessary if liver damage is extensive.
What promise do clinical trials hold for treatment of Wilson disease?
A newer copper chelating agent currently being investigated is tetrathiomolybdate. The hope is that it will prove to have fewer side effects than penicillamine, yet be more effective than Trientine.
What is the prognosis for Wilson disease?
Without treatment, Wilson disease is always fatal. With treatment, symptoms may continue to worsen for the first six to eight weeks.
What is treatment of Wilson disease?
Treatment of WD revolves around the process of copper chelation. A chelating agent binds to excess copper in the bloodstream so that it can be excreted from the body.
Is there a cure for Wilson disease?
Sadly, there is no cure to Wilson's disease. : (
What types of professional are involved in treatment of Wilson disease?
A gastroenterologist will treat and monitor liver disease, while a neurologist and psychiatrist (or neuropsychiatrist) should evaluate and treat neuropsychiatric symptoms.
Is zinc used to treat Wilson disease?
Treatment with zinc acetate is also an effective way to remove excess copper from the body.
Is a liver transplant a treatment for Wilson disease?
Patients may be given a liver transplant in the event of liver failure as a complication of WD.
Can you die from Wilson's disease?
Yes, if not treated, Wilson disease may cause death.
What is the prognosis for patients with Wilson disease?
The earlier in the course of the disorder that treatment is started, the more beneficial the effects will be. For others who have a more severe form of the disease, only modest improvements may be seen.
What is Wilson's Disease?
it is a rare diorder of abnormal copper metabolism and is characterised by: hepatolenticular degeneration. copper get deposited in abnormal amounts in liver and lenticular nucleus of brain leading to necrosis of liver and brain. low level of copper and ceruloplasmin in plasma with increased excretion of copper in urine, copper deposition in kidneys causes renal damage. causes: failure in the synthesis of ceruloplasmin. excess copper in plasma. reduced intestinal excretion of copper. treatment: penicillamine.
Is Wilson disease common?
because Wilson disease is so rare, diagnosis is often unfortunately delayed.
