The persistence of jaundice beyond the second week in a newborn with clay-colored stools is a sure sign of obstruction to the flow of bile. An immediate evaluation that includes blood tests and imaging of the biliary system will confirm the diagnosis.
Biliary atresia is the most common lethal liver disease in children, occurring once every 10,000-15,000 live births. Half of all liver transplants are done for this reason.
No, there is a 30-40% chance of Down Syndrome when duodenal atresia is diagnosed.
It is possible that a viral infection is responsible for this disease, but evidence is not yet convincing. The cause remains unknown.
The main treatment for biliary atresia is a surgical procedure called the Kasai procedure, which involves connecting the liver directly to the small intestine to allow bile to flow. If the Kasai procedure is not successful or if complications arise, a liver transplant may be needed. In addition, some medications and nutritional support may be required to manage symptoms and support liver function.
The specific cause of this birth defect is unknown, so all that women can do is to practice the many general preventive measures, even before they conceive.
* Anal atresia -- congenital absence of a hole at the bottom end of the intestine. Also called imperforate anus. * Aortic atresia -- congenital absence of the normal valvular opening into the aorta. * Biliary atresia -- absence of the major bile ducts. * Choanal atresia -- congenital failure of one or both nasal passages to open. * Esophageal atresia -- a birth defect in which part of esophagus is not hollow. * Intestinal atresia -- obliteration of the hollow of the small intestine, involving the ileum (50% of cases) or the jejunum or duodenum. * Laryngeal atresia -- congenital failure of the laryngeal opening to develop, resulting in partial or total obstruction at or just above or below the glottis. * Pulmonary atresia -- congenital absence of the pulmonary valve opening in the heart. * Tricuspid atresia -- congenital lack of the tricuspid valve opening. * Vaginal atresia -- congenital occlusion of the vagina or subsequence adhesion (sticking together) of the walls of the vagina occluding it.
Blood tests strongly suggest the correct diagnosis, but a liver biopsy is needed for confirmation. It is also usually necessary to x ray the biliary system to look for other causes of obstruction.
Atresia is a term related to cavities. Atresia is the condition in which a tube is blocked, or absent.
After two weeks the normal jaundice of the newborn will not disappear.the stools will probably be clay-colored.the child's abdomen will begin to swell.Nearly all untreated children will die of liver failure within two years.
AIR IN BILIARY SYSTEM. AIR IN BILIARY SYSTEM.
Primary biliary cirrhosis is the gradual destruction of the biliary system for unknown reasons.
biliary apparatus collects bile from live and store it in gall bladder